Severe myoclonic epilepsy in infants (SME) is one of the most malignant epileptic
syndromes recognized in the latest classification of epileptic syndromes. The clinical details
and electroencephalographic (EEG) characteristics have been elucidated by Dravet et al.
The diagnosis of SME depends largely on the combination of clinical and EEG
manifestations at different ages, of which the presence of myoclonic seizures appears to be
the most important. However, because of the inclusion of different types of myoclonic attack …