[HTML][HTML] LRH-1 mitigates intestinal inflammatory disease by maintaining epithelial homeostasis and cell survival

JR Bayrer, H Wang, R Nattiv, M Suzawa… - Nature …, 2018 - nature.com
JR Bayrer, H Wang, R Nattiv, M Suzawa, HS Escusa, RJ Fletterick, OD Klein, DD Moore
Nature communications, 2018nature.com
Epithelial dysfunction and crypt destruction are defining features of inflammatory bowel
disease (IBD). However, current IBD therapies targeting epithelial dysfunction are lacking.
The nuclear receptor LRH-1 (NR5A2) is expressed in intestinal epithelium and thought to
contribute to epithelial renewal. Here we show that LRH-1 maintains intestinal epithelial
health and protects against inflammatory damage. Knocking out LRH-1 in murine intestinal
organoids reduces Notch signaling, increases crypt cell death, distorts the cellular …
Abstract
Epithelial dysfunction and crypt destruction are defining features of inflammatory bowel disease (IBD). However, current IBD therapies targeting epithelial dysfunction are lacking. The nuclear receptor LRH-1 (NR5A2) is expressed in intestinal epithelium and thought to contribute to epithelial renewal. Here we show that LRH-1 maintains intestinal epithelial health and protects against inflammatory damage. Knocking out LRH-1 in murine intestinal organoids reduces Notch signaling, increases crypt cell death, distorts the cellular composition of the epithelium, and weakens the epithelial barrier. Human LRH-1 (hLRH-1) rescues epithelial integrity and when overexpressed, mitigates inflammatory damage in murine and human intestinal organoids, including those derived from IBD patients. Finally, hLRH-1 greatly reduces disease severity in T-cell-mediated murine colitis. Together with the failure of a ligand-incompetent hLRH-1 mutant to protect against TNFα-damage, these findings provide compelling evidence that hLRH-1 mediates epithelial homeostasis and is an attractive target for intestinal disease.
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